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5.
Cir Esp ; 82(2): 125-7, 2007 Aug.
Artigo em Espanhol | MEDLINE | ID: mdl-17785148

RESUMO

Leiomyomatosis peritonealis disseminata is an uncommon condition characterized by subperitoneal proliferation of benign nodules mainly composed of benign smooth muscle cells. This entity generally appears in premenopausal women and hormonal influences may play a role in its pathogenesis. The macroscopic appearance mimics peritoneal carcinomatosis. The characteristic clinical course is asymptomatic and diagnosis is only feasible after microscopic examination. To date, less than 100 cases have been reported in the literature. We report the case of a 40-year-old woman who underwent surgery in our department.


Assuntos
Leiomiomatose/diagnóstico por imagem , Leiomiomatose/patologia , Neoplasias de Tecido Conjuntivo/diagnóstico por imagem , Neoplasias de Tecido Conjuntivo/patologia , Adulto , Feminino , Humanos , Leiomiomatose/cirurgia , Imageamento por Ressonância Magnética , Músculo Liso/patologia , Músculo Liso/cirurgia , Neoplasias de Tecido Conjuntivo/cirurgia , Peritônio/diagnóstico por imagem , Peritônio/patologia , Peritônio/cirurgia , Tomografia Computadorizada por Raios X
6.
Cir. Esp. (Ed. impr.) ; 82(2): 125-127, ago. 2007. ilus
Artigo em Es | IBECS | ID: ibc-055778

RESUMO

La leiomiomatosis peritoneal diseminada es una entidad rara que se caracteriza por la proliferación subendotelial de nódulos básicamente compuestos de células de músculo liso. Aparece de forma general en mujeres premenopáusicas y su patogenia tiene gran influencia hormonal. Simula macroscópicamente una carcinomatosis peritoneal. De forma característica cursa de forma indolente y el diagnóstico es sólo posible tras el examen histológico. Se han descrito menos de 100 casos en la literatura científica hasta la fecha. Presentamos un caso de una paciente de 40 años intervenida en nuestro servicio (AU)


Leiomyomatosis peritonealis disseminata is an uncommon condition characterized by subperitoneal proliferation of benign nodules mainly composed of benign smooth muscle cells. This entity generally appears in premenopausal women and hormonal influences may play a role in its pathogenesis. The macroscopic appearance mimics peritoneal carcinomatosis. The characteristic clinical course is asymptomatic and diagnosis is only feasible after microscopic examination. To date, less than 100 cases have been reported in the literature. We report the case of a 40-year-old woman who underwent surgery in our department (AU)


Assuntos
Feminino , Adulto , Humanos , Leiomiomatose/diagnóstico , Neoplasias Peritoneais/diagnóstico , Tomografia Computadorizada por Raios X , Imageamento por Ressonância Magnética , Diagnóstico Diferencial , Leiomiomatose/patologia , Biópsia , Neoplasias Peritoneais/patologia
7.
Cir Esp ; 81(2): 102-4, 2007 Feb.
Artigo em Espanhol | MEDLINE | ID: mdl-17306128

RESUMO

Surgery in hemophilic patients is a challenge for the general surgeon. Hemophilic pseudotumor is a rare complication occurring in 1-2% of hemophiliacs and affecting mainly patients with severe disease or those who have developed antibodies to factor VIII or IX. A number of alternatives are available for the management of these tumors, including conservative treatment, surgical removal, percutaneous drainage, embolization, and external radiation. The only definitive treatment is surgical excision. We report a case of hemophilic pseudotumor of the pelvic bone. Treatment consisted of surgical resection after arterial embolization using factor replacement to achieve hemostasis.


Assuntos
Doenças Ósseas/etiologia , Doenças Ósseas/cirurgia , Hemofilia A/complicações , Ossos Pélvicos , Adulto , Embolização Terapêutica , Humanos , Masculino
8.
Cir. Esp. (Ed. impr.) ; 81(2): 102-104, feb.2007. ilus
Artigo em Es | IBECS | ID: ibc-051751

RESUMO

La cirugía en pacientes hemofílicos es un reto para el cirujano general. El seudotumor hemofílico es una complicación rara que se presenta en el 1-2% de los hemofílicos y afecta principalmente a las formas graves y a los pacientes que han desarrollado anticuerpos contra el factor VIII o IX. Existen varias alternativas para el manejo de estos tumores: tratamiento conservador, cirugía de exéresis, punción percutánea, embolización e irradiación externa. La exéresis quirúrgica es el único tratamiento definitivo. Presentamos un caso de seudotumor hemofílico pelviano tratado quirúrgicamente previa embolización arterial y usando infusión de factor durante la cirugía para una buena hemostasia


Surgery in hemophilic patients is a challenge for the general surgeon. Hemophilic pseudotumor is a rare complication occurring in 1-2% of hemophiliacs and affecting mainly patients with severe disease or those who have developed antibodies to factor VIII or IX. A number of alternatives are available for the management of these tumors, including conservative treatment, surgical removal, percutaneous drainage, embolization, and external radiation. The only definitive treatment is surgical excision. We report a case of hemophilic pseudotumor of the pelvic bone. Treatment consisted of surgical resection after arterial embolization using factor replacement to achieve hemostasis


Assuntos
Masculino , Adulto , Humanos , Hemofilia B/complicações , Hemostasia Cirúrgica/métodos , Procedimentos Cirúrgicos Operatórios/efeitos adversos , Granuloma de Células Plasmáticas/cirurgia , Complicações Pós-Operatórias/cirurgia , Embolização Terapêutica , Fator VIII , Fator IX
9.
Cir Esp ; 80(5): 337-8, 2006 Nov.
Artigo em Espanhol | MEDLINE | ID: mdl-17192211

RESUMO

Esophageal lipomas are uncommon benign tumors. The main symptom of this type of tumor is dysphagia due to esophageal obstruction. The diagnostic studies of choice are endoscopy, radiological investigation with contrast administration, computed tomography, and echoendoscopy. We present an unusual case of giant pediculated esophageal lipoma which manifested clinically with dysphagia. Management was surgical.


Assuntos
Neoplasias Esofágicas/diagnóstico , Lipoma/diagnóstico , Idoso , Procedimentos Cirúrgicos do Sistema Digestório/métodos , Neoplasias Esofágicas/cirurgia , Esofagoscopia , Humanos , Lipoma/cirurgia , Imageamento por Ressonância Magnética , Masculino , Tomografia Computadorizada por Raios X , Resultado do Tratamento
10.
Cir. Esp. (Ed. impr.) ; 80(5): 337-338, nov. 2006. ilus
Artigo em Es | IBECS | ID: ibc-049171

RESUMO

Los lipomas esofágicos son tumores benignos raros. El síntoma principal, en caso de que lo haya, es en forma de disfagia secundaria a la obstrucción esofágica. Los estudios diagnósticos de elección son la endoscopia, el examen radiológico con contraste, la tomografía computarizada y la ecoendoscopia. Presentamos un caso inusual de lipoma esofágico gigante y pediculado que se manifestó clínicamente con disfagia, cuyo abordaje fue quirúrgico (AU)


Esophageal lipomas are uncommon benign tumors. The main symptom of this type of tumor is dysphagia due to esophageal obstruction. The diagnostic studies of choice are endoscopy, radiological investigation with contrast administration, computed tomography, and echoendoscopy. We present an unusual case of giant pediculated esophageal lipoma which manifested clinically with dysphagia. Management was surgical (AU)


Assuntos
Masculino , Feminino , Humanos , Lipoma/diagnóstico , Lipoma/cirurgia , Tomografia Computadorizada de Emissão/métodos , Endoscopia/métodos , Diagnóstico Diferencial , Endossonografia/métodos , Endossonografia , Meios de Contraste/análise , Lipomatose/complicações , Lipomatose/diagnóstico , Lipomatose/cirurgia
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